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https://repository.monashhealth.org/monashhealthjspui/handle/1/46889| Title: | Cardiopulmonary bypass in a child with erythropoietic protoporphyria. | Authors: | Pathman L.;Bennett M.;d'Udekem Y.;Phillips R. | Institution: | (Pathman, Bennett, d'Udekem, Phillips) The Royal Children's Hospital, Melbourne, Australia (d'Udekem) Children's National Hospital, Washington, DC, United States (Phillips) Monash Medical Centre, Melbourne, Australia (Phillips) Murdoch Children's Research Institute, Melbourne, Australia |
Issue Date: | 4-Mar-2022 | Publisher: | John Wiley and Sons Inc | Place of publication: | Australia | Publication information: | Australasian Journal of Dermatology. 63(1) (pp e60-e62), 2022. Date of Publication: February 2022. | Journal: | Australasian Journal of Dermatology | Abstract: | Children with erythropoietic porphyria are generally under the care of paediatric dermatologists. When these children undergo major surgery, they are at risk of unusual complications due to their photosensitivity. Dermatologists may be consulted prior to surgery for advice. We describe a case of a child with erythropoietic porphyria undergoing open heart surgery, utilising an exchange transfusion alongside other strategies to minimise the risk of photosensitivity-induced haemolysis.Copyright © 2021 Australasian College of Dermatologists. | DOI: | http://monash.idm.oclc.org/login?url=https://dx.doi.org/10.1111/ajd.13751 | PubMed URL: | 34817070 [https://www.ncbi.nlm.nih.gov/pubmed/?term=34817070] | URI: | https://repository.monashhealth.org/monashhealthjspui/handle/1/46889 | Type: | Article | Subjects: | allele anesthesia cardiopulmonary bypass clinical clinical decision making consultation elective surgery erythema erythropoietic protoporphyria/di erythropoietic protoporphyria/th [Therapy] exchange blood transfusion gene mutation heart surgery heart ventricle septum defect/su [Surgery] hospital admission hospital discharge intensive care near infrared spectroscopy open surgery pediatrics photosensitivity postoperative period sun exposure swelling dexmedetomidine/pv [Special Situation for Pharmacovigilance] fentanyl/pv [Special Situation for Pharmacovigilance] pancuronium/pv [Special Situation for Pharmacovigilance] sevoflurane/pv [Special Situation for Pharmacovigilance] tranexamic acid/pv [Special Situation for Pharmacovigilance] |
Type of Clinical Study or Trial: | Case series or case report |
| Appears in Collections: | Articles |
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